Interstitial lung disease (ILD) is a common manifestation of systemic sclerosis (SSc) and mainly
encountered in patients with diffuse disease and/or anti-topoisomerase 1 antibodies. ILD …

Autoimmune manifestations have long been perceived as paradoxical in patients with
primary immune deficiencies (PID). However, a defect in the mechanisms of control of self-reactive …

Pulmonary arterial hypertension is characterized by a remodeling of pulmonary arteries with
endothelial cell, fibroblast, and vascular smooth muscle cell activation and proliferation. …

Scleroderma renal crisis (SRC) is a major complication in patients with systemic sclerosis (SSc).
It is characterized by malignant hypertension and oligo/anuric acute renal failure. SRC …

Rationale: Pulmonary arterial hypertension (PAH) may be classified as idiopathic (IPAH) or
familial (FPAH) or associated with various conditions and exposures such as …

Scleroderma renal crisis (SRC) is characterized by malignant hypertension and oligo-anuric
acute renal failure. It occurs in 5% of patients with systemic sclerosis (SSc), particularly in …

Anti-endothelial cell antibodies (AECAs) have been identified in patients with systemic
sclerosis (SSc) with and without pulmonary arterial hypertension (PAH) and in patients with …

To better assess the efficacy and safety of rituximab in adults' warm antibody autoimmune
hemolytic anemia (wAIHA), we conducted a retrospective study including 27 adults (mean age …

Background The landscape of polyarteritis nodosa (PAN) has substantially changed during
the last decades. Recent data regarding causes, characteristics, and prognosis of systemic …

Introduction Our objective was to evaluate characteristics, treatment and outcome of vasculitis
associated with myelodysplastic syndrome (MDS) and chronic myelomonicytic leukemia (…