User profiles for Francis X. McCormack

Francis X. McCormack

Division of Pulmonary, Critical Care and Sleep Medicine, The University of Cincinnati
Verified email at uc.edu
Cited by 20426

[HTML][HTML] The pulmonary collectins, SP-A and SP-D, orchestrate innate immunity in the lung

FX McCormack, JA Whitsett - The Journal of clinical …, 2002 - Am Soc Clin Investig
… This work was supported by NIH grants to FX McCormack (HL-61612) and JA Whitsett (HL-61646),
and by a Merit Grant to McCormack from the Department of Veterans Affairs, …

Lymphangioleiomyomatosis: a clinical update

FX McCormack - Chest, 2008 - Elsevier
Lymphangioleiomyomatosis (LAM) is a rare, cystic lung disease that is associated with
mutations in tuberous sclerosis genes, renal angiomyolipomas, lymphatic spread, and …

[HTML][HTML] Lymphangioleiomyomatosis—a wolf in sheep's clothing

EP Henske, FX McCormack - The Journal of clinical …, 2012 - Am Soc Clin Investig
Lymphangioleiomyomatosis (LAM) is a rare progressive lung disease of women. LAM is
caused by mutations in the tuberous sclerosis genes, resulting in activation of the mTOR …

[HTML][HTML] Tuberous sclerosis complex diagnostic criteria update: recommendations of the 2012 International Tuberous Sclerosis Complex Consensus Conference

…, J Roth, H Wang, H Weiner, FX McCormack… - Pediatric …, 2013 - Elsevier
Background Tuberous sclerosis complex is highly variable in clinical presentation and
findings. Disease manifestations continue to develop over the lifetime of an affected individual. …

[HTML][HTML] Sirolimus for angiomyolipoma in tuberous sclerosis complex or lymphangioleiomyomatosis

JJ Bissler, FX McCormack, LR Young… - … England Journal of …, 2008 - Mass Medical Soc
Background Angiomyolipomas in patients with the tuberous sclerosis complex or sporadic
lymphangioleiomyomatosis are associated with mutations in tuberous sclerosis genes …

[HTML][HTML] Efficacy and safety of sirolimus in lymphangioleiomyomatosis

FX McCormack, Y Inoue, J Moss… - … England Journal of …, 2011 - Mass Medical Soc
Background Lymphangioleiomyomatosis (LAM) is a progressive, cystic lung disease in
women; it is associated with inappropriate activation of mammalian target of rapamycin (mTOR) …

[HTML][HTML] Tuberous sclerosis complex surveillance and management: recommendations of the 2012 International Tuberous Sclerosis Complex Consensus Conference

…, J Roth, H Wang, H Weiner, FX McCormack… - Pediatric …, 2013 - Elsevier
Background Tuberous sclerosis complex is a genetic disorder affecting every organ system,
but disease manifestations vary significantly among affected individuals. The diverse and …

[HTML][HTML] Updated international tuberous sclerosis complex diagnostic criteria and surveillance and management recommendations

…, JC Kingswood, TK Knilans, FX McCormack… - Pediatric Neurology, 2021 - Elsevier
Background Tuberous sclerosis complex (TSC) is an autosomal dominant genetic disease
affecting multiple body systems with wide variability in presentation. In 2013, Pediatric …

The NHLBI lymphangioleiomyomatosis registry: characteristics of 230 patients at enrollment

…, A Taveira-DaSilva, FX McCormack… - American journal of …, 2006 - atsjournals.org
Rationale: Pulmonary lymphangioleiomyomatosis is a progressive cystic lung disease that
is associated with infiltration of atypical smooth muscle–like cells. Previous descriptions of …

[HTML][HTML] Surfactant proteins A and D inhibit the growth of Gram-negative bacteria by increasing membrane permeability

…, JH Fisher, KS Kim, FX McCormack - The Journal of …, 2003 - Am Soc Clin Investig
The pulmonary collectins, surfactant proteins A (SP-A) and D (SP-D), have been reported to
bind lipopolysaccharide (LPS), opsonize microorganisms, and enhance the clearance of …