Chest physiotherapy with positive airway pressure: a pilot study of short-term effects on sputum clearance in patients with cystic fibrosis and severe airway obstruction

…, G Polese, L Zanolla, BM Assael, C Braggion - Respiratory …, 2006 - rc.rcjournal.com
BACKGROUND: The periodic administration of positive airway pressure combined with directed
cough could aid mucus clearance in patients with cystic fibrosis (CF) and severe airway …

[HTML][HTML] Serratia marcescens outbreak in a neonatal intensive care unit: crucial role of implementing hand hygiene among external consultants

…, L Lega, S Campana, KP Biermann, C Braggion… - BMC infectious …, 2015 - Springer
Background Serratia marcescens represents an important pathogen involved in hospital
acquired infections. Outbreaks are frequently reported and are difficult to eradicate. The aim of …

Two CFTR mutations within codon 970 differently impact on the chloride channel functionality

…, E Vanderhelst, V Terlizzi, C Braggion… - Human …, 2019 - Wiley Online Library
Pharmacological rescue of mutant cystic fibrosis transmembrane conductance regulator (CFTR)
in cystic fibrosis (CF) depends on the specific defect caused by different mutation classes…

[HTML][HTML] Cystic fibrosis screen positive inconclusive diagnosis (CFSPID): Experience in Tuscany, Italy

…, R Buzzetti, C Centrone, L Zavataro, C Braggion - Journal of Cystic …, 2019 - Elsevier
Objective The implementation of cystic fibrosis (CF) newborn screening (NBS) has led to
identification of infants with a positive NBS test but inconclusive diagnosis classified as “CF …

[HTML][HTML] Methicillin-resistant Staphylococcus aureus eradication in cystic fibrosis patients: A randomized multicenter study

…, F Miselli, E Camera, L Zavataro, C Braggion… - PLoS …, 2019 - journals.plos.org
Background Few studies, based on a limited number of patients using non-uniform therapeutic
protocols, have analyzed Methicillin-resistant Staphylococcus aureus (MRSA) eradication…

[HTML][HTML] Clinical expression of cystic fibrosis in a large cohort of Italian siblings

…, D Salvatore, A Angioni, A Bisogno, C Braggion… - BMC Pulmonary …, 2018 - Springer
Background A clinical heterogeneity was reported in patients with Cystic Fibrosis (CF) with
the same CFTR genotype and between siblings with CF. Methods We investigated all clinical …

The prevalence of anxiety and depression in Italian patients with cystic fibrosis and their caregivers

…, C Risso, P Tabarini, C Braggion… - Pediatric …, 2016 - Wiley Online Library
Background: Cystic fibrosis, like other chronic diseases, is a risk factor for the development
of elevated symptoms of depression and anxiety. The objective of this study was to …

[HTML][HTML] Trans-heterozygosity for mutations enhances the risk of recurrent/chronic pancreatitis in patients with Cystic Fibrosis

…, L Da Sacco, F Alghisi, A Angiolillo, C Braggion… - Molecular …, 2018 - Springer
Background Recurrent (RP) and chronic pancreatitis (CP) may complicate Cystic Fibrosis (CF).
It is still unknown if mutations in genes involved in the intrapancreatic activation of trypsin …

Travel-Associated Burkholderia pseudomallei Infection (Melioidosis) in a Patient with Cystic Fibrosis: A Case Report

…, G Cazzola, A Petrucca, C Braggion - Clinical Infectious …, 2001 - academic.oup.com
In September 1997, a 25-year-old Italian woman with cystic fibrosis (CF) spent 3 weeks in
Thailand. In August 1998, her pulmonary function rapidly declined, with productive cough and …

Effectivenesss of ivacaftor in severe cystic fibrosis patients and non‐G551D gating mutations

…, V Carnovale, P Iacotucci, C Braggion… - Pediatric …, 2019 - Wiley Online Library
Background Ivacaftor is a significant innovation in the treatment of cystic fibrosis (CF) with
gating mutations. A substantial percentage of patients with CF have severe lung involvement, …