Deficit of osteoprotegerin release by osteoblasts from a patient with cystic fibrosis

Eur Respir J. 2012 Mar;39(3):780-1. doi: 10.1183/09031936.00104111.
No abstract available

Publication types

  • Case Reports
  • Letter
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adenylyl Cyclases / metabolism
  • Adult
  • Cells, Cultured
  • Colforsin / pharmacology
  • Cystic Fibrosis / metabolism*
  • Cystic Fibrosis Transmembrane Conductance Regulator / agonists
  • Cystic Fibrosis Transmembrane Conductance Regulator / genetics
  • Genistein / pharmacology
  • Humans
  • Male
  • Osteoblasts / metabolism*
  • Osteoprotegerin / metabolism*
  • Tumor Necrosis Factor-alpha / pharmacology

Substances

  • Osteoprotegerin
  • Tumor Necrosis Factor-alpha
  • Cystic Fibrosis Transmembrane Conductance Regulator
  • Colforsin
  • Genistein
  • Adenylyl Cyclases